Urrets-Zavalia syndrome after deep anterior lamellar keratoplasty
Sindrom Urets-Zavalia nastao posle duboke prednje lamelarne keratoplastike
Apstrakt
Introduction. Urrets-Zavalia syndrome is an uncommon complication of the deep anterior lamellar keratoplasty in keratoconus. The manifestations of this syndrome are an irreversible mydriasis, iris atrophy and secondary glaucoma. Case report. Deep anterior lamellar keratoplasty was done for keratoconus with a presumably healed corneal hydrops in a 21-year-old Caucasian man. The graft remained clear, but the surgery was complicated by a fixed, dilated pupil, patches of iris atrophy, ectropium of the iris pigment layer and glaukomflecken in the lens. Conclusion. Although safer than penetrating keratoplasty, the deep anterior lamellar corneal transplantation is not devoid of complications. Urrets-Zavalia syndrome can be avoided by not trying to secure an unhealed Descemet's membrane with air. Instead, a new Descemet's membrane transplanted within a penetrating graft is a safer choice.
Uvod. Sindrom Urets-Zavalije je neuobičajena komplikacija posle operacije keratokonusa metodom duboke prednje lamelarne keratoplastike. Manifestacije ovog sindroma su trajna midrijaza, atrofija dužice i sekundarni glaukom. Prikaz bolesnika. Kod bolesnika starog 21 godinu, urađena je duboka prednja lamelarna keratoplastika sa keratokonusom i naizgled zaceljenim hidropsom rožnjače. Kalem je ostao providan, ali se operacija komplikovala trajnom midrijazom, poljima atrofije dužice, izvrnutim rubom pigmentnog sloja dužice i mrljastim zamućenjima ispod prednje kapsule sočiva (glaukomflecken). Zaključak. Mada bezbednija od perforativne keratoplastike, duboka prednja lamelarna transplantacija rožnjače nije bez komplikacija. Sindrom Urets-Zavalije može se izbeći ako se umesto zaptivanja otvora u Descemetovoj membrani pomoću vazduha, presadi nova Descemetova membrana zajedno sa kalemom, tehnikom perforativne keratoplastike.
Ključne reči:
corneal transplantation / keratoconus / postoperative complications / syndrome / transplantacija rožnjače / keratokonus / postoperativne komplikacije / sindromIzvor:
Vojnosanitetski pregled, 2016, 73, 10, 973-975Izdavač:
- Vojnomedicinska akademija - Institut za naučne informacije, Beograd
DOI: 10.2298/VSP141109088J
ISSN: 0042-8450
WoS: 000388261500013
Scopus: 2-s2.0-84989318621
Kolekcije
Institucija/grupa
Stomatološki fakultetTY - JOUR AU - Jovanović, Vesna AU - Nikolić, Ljubiša PY - 2016 UR - https://smile.stomf.bg.ac.rs/handle/123456789/2079 AB - Introduction. Urrets-Zavalia syndrome is an uncommon complication of the deep anterior lamellar keratoplasty in keratoconus. The manifestations of this syndrome are an irreversible mydriasis, iris atrophy and secondary glaucoma. Case report. Deep anterior lamellar keratoplasty was done for keratoconus with a presumably healed corneal hydrops in a 21-year-old Caucasian man. The graft remained clear, but the surgery was complicated by a fixed, dilated pupil, patches of iris atrophy, ectropium of the iris pigment layer and glaukomflecken in the lens. Conclusion. Although safer than penetrating keratoplasty, the deep anterior lamellar corneal transplantation is not devoid of complications. Urrets-Zavalia syndrome can be avoided by not trying to secure an unhealed Descemet's membrane with air. Instead, a new Descemet's membrane transplanted within a penetrating graft is a safer choice. AB - Uvod. Sindrom Urets-Zavalije je neuobičajena komplikacija posle operacije keratokonusa metodom duboke prednje lamelarne keratoplastike. Manifestacije ovog sindroma su trajna midrijaza, atrofija dužice i sekundarni glaukom. Prikaz bolesnika. Kod bolesnika starog 21 godinu, urađena je duboka prednja lamelarna keratoplastika sa keratokonusom i naizgled zaceljenim hidropsom rožnjače. Kalem je ostao providan, ali se operacija komplikovala trajnom midrijazom, poljima atrofije dužice, izvrnutim rubom pigmentnog sloja dužice i mrljastim zamućenjima ispod prednje kapsule sočiva (glaukomflecken). Zaključak. Mada bezbednija od perforativne keratoplastike, duboka prednja lamelarna transplantacija rožnjače nije bez komplikacija. Sindrom Urets-Zavalije može se izbeći ako se umesto zaptivanja otvora u Descemetovoj membrani pomoću vazduha, presadi nova Descemetova membrana zajedno sa kalemom, tehnikom perforativne keratoplastike. PB - Vojnomedicinska akademija - Institut za naučne informacije, Beograd T2 - Vojnosanitetski pregled T1 - Urrets-Zavalia syndrome after deep anterior lamellar keratoplasty T1 - Sindrom Urets-Zavalia nastao posle duboke prednje lamelarne keratoplastike VL - 73 IS - 10 SP - 973 EP - 975 DO - 10.2298/VSP141109088J ER -
@article{ author = "Jovanović, Vesna and Nikolić, Ljubiša", year = "2016", abstract = "Introduction. Urrets-Zavalia syndrome is an uncommon complication of the deep anterior lamellar keratoplasty in keratoconus. The manifestations of this syndrome are an irreversible mydriasis, iris atrophy and secondary glaucoma. Case report. Deep anterior lamellar keratoplasty was done for keratoconus with a presumably healed corneal hydrops in a 21-year-old Caucasian man. The graft remained clear, but the surgery was complicated by a fixed, dilated pupil, patches of iris atrophy, ectropium of the iris pigment layer and glaukomflecken in the lens. Conclusion. Although safer than penetrating keratoplasty, the deep anterior lamellar corneal transplantation is not devoid of complications. Urrets-Zavalia syndrome can be avoided by not trying to secure an unhealed Descemet's membrane with air. Instead, a new Descemet's membrane transplanted within a penetrating graft is a safer choice., Uvod. Sindrom Urets-Zavalije je neuobičajena komplikacija posle operacije keratokonusa metodom duboke prednje lamelarne keratoplastike. Manifestacije ovog sindroma su trajna midrijaza, atrofija dužice i sekundarni glaukom. Prikaz bolesnika. Kod bolesnika starog 21 godinu, urađena je duboka prednja lamelarna keratoplastika sa keratokonusom i naizgled zaceljenim hidropsom rožnjače. Kalem je ostao providan, ali se operacija komplikovala trajnom midrijazom, poljima atrofije dužice, izvrnutim rubom pigmentnog sloja dužice i mrljastim zamućenjima ispod prednje kapsule sočiva (glaukomflecken). Zaključak. Mada bezbednija od perforativne keratoplastike, duboka prednja lamelarna transplantacija rožnjače nije bez komplikacija. Sindrom Urets-Zavalije može se izbeći ako se umesto zaptivanja otvora u Descemetovoj membrani pomoću vazduha, presadi nova Descemetova membrana zajedno sa kalemom, tehnikom perforativne keratoplastike.", publisher = "Vojnomedicinska akademija - Institut za naučne informacije, Beograd", journal = "Vojnosanitetski pregled", title = "Urrets-Zavalia syndrome after deep anterior lamellar keratoplasty, Sindrom Urets-Zavalia nastao posle duboke prednje lamelarne keratoplastike", volume = "73", number = "10", pages = "973-975", doi = "10.2298/VSP141109088J" }
Jovanović, V.,& Nikolić, L.. (2016). Urrets-Zavalia syndrome after deep anterior lamellar keratoplasty. in Vojnosanitetski pregled Vojnomedicinska akademija - Institut za naučne informacije, Beograd., 73(10), 973-975. https://doi.org/10.2298/VSP141109088J
Jovanović V, Nikolić L. Urrets-Zavalia syndrome after deep anterior lamellar keratoplasty. in Vojnosanitetski pregled. 2016;73(10):973-975. doi:10.2298/VSP141109088J .
Jovanović, Vesna, Nikolić, Ljubiša, "Urrets-Zavalia syndrome after deep anterior lamellar keratoplasty" in Vojnosanitetski pregled, 73, no. 10 (2016):973-975, https://doi.org/10.2298/VSP141109088J . .